Fallbericht: Moya-Moya-Erkrankung

Moyamoya Disease – Case Report. Moyamoya disease is a more common disease in Asian population and well discussed since 1957. Because of the continuously increasing population of people with migration background, this disease is getting a topical subject in European countries. Characterized by occlusion of the distal carotid arteries, it is a progressive disease with a fragile network of basal collateral vessels. The angiographic appearance of the brain showing a rete mirabile is typical. The clinical aspect of each patient is different depending on age and stage of the disease. Vertigo, cephalea, passager hemiparesis or aphasia, as well as seizures are common. Cerebral hemorrhage is uncommon in children. Genesis is still unknown. Sometimes moyamoya is associated with neurofibromatosis type I, pituitary tumors, cardiac dysfunctions, or haematological disorders like sickle-cell anemia. A recent case in our pediatric neurosurgery unit with good therapeutical results was the reason for writing this paper. J Neurol Neurochir Psychiatr 2015; 16 (2): 72–5.